Sep 11 2008 Background and Purpose We describe the clinical diagnostic and outcome features of a cohort of white patients with idiopathic moyamoya disease treated in a German institution. Methods Our cohort included 21 white patients with moyamoya disease. Clinical and diagnostic features were obtained by retrospective chart review follow up information and
Moyamoya disease staging system. The staging system for moyamoya disease first described by Suzuki and Takaku in their seminal 1969 article 9 is still in use today. Formally the staging refers to findings on conventional angiography although there are efforts to apply similar systems to MR angiography 10 .. Suzuki stage appears to correlate with collateralization in children
The origin of moyamoya disease remains unknown. The onset of the angiographically apparent changes of typical moyamoya disease occurs in childhood but de novo development of the disease has not been confirmed angiographically. The authors report on a case of de novo development of moyamoya disease in a middle aged female whose cerebral angiography
Evidence on the natural angiographic course of moyamoya disease MMD is lacking. It takes about 6 months for waiting for revascularisation surgery. The issue of when to perform subtraction angiography DSA for follow up remains unclear. We investigated the natural course of MMD by DSA and attempted to determine the best interval to perform the follow up DSA. This is a
Objective To identify associated risk factors for the angiographic outcomes after direct and combined bypass surgery in moyamoya disease MMD .Methods All direct and combined bypass procedures performed from June 2009 to May 2015 were screened in this prospective cohort study. Patients who acquired presurgical and follow up catheter angiography were
Oct 01 1997 The mean lag time between the first clinical manifestation and the angiographic diagnosis was about 2 years. A medical treatment vasodilators antiplatelet agents calcium channel blockers was followed by 21 patients while five cases underwent a surgical revascularization. Moyamoya disease MMD is a rare occlusive cerebral vasculopathy
Mar 26 2015 Epidemiology. First described in Japan moyamoya has now been identified in patients worldwide. 6 Although historically considered more prevalent in the Asian population it affects individuals of many ethnic backgrounds and there is increasing awareness of this disease in Europe and North America. 7 In Japan it is the most common pediatric cerebrovascular
To clarify the differences between childhood onset moyamoya disease and that with onset in adulthood we studied the clinical course and angiographic findings of adult patients over 20 years of age with moyamoya disease of childhood onset up to 15 years of age . The clinical course in 25 patients could be assessed. The follow up period was 5–27 years. Neurological
OBJECT The present study aimed to clarify the incidence and clinical features of disease progression in adult moyamoya disease MMD patients with Graves disease GD for better management of these patients. METHODS During the past 18 years 320 adult Chinese patients at West China Hospital were diagnosed with MMD and 29 were also diagnosed with GD. A
Clinical and cerebral angiographic evolutions of idiopathic progressive occlusive disease of the circle of Willis moyamoya disease in children. Fukuyama Y Umezu R. In 33 pediatric cases of idiopathic progressive occlusive disease of the circle of Willis so called moyamoya disease clinical features and CAG findings were studied with
Moyamoya disease is a neurovascular pathology characterized by the progressive stenosis of the supraclinoidal portion of the internal carotid artery and its 2 main branches the anterior cerebral artery ACA and middle cerebral artery in their proximal segments. 1 –3 During the evolution of the pathology the development of collaterals maintains a minimal perfusion to the
Sep 09 2020 Moyamoya disease is a unique cerebrovascular entity characterized by progressive large intracranial artery narrowing and the development of prominent small vessel collaterals. The latter produces a characteristic smoky appearance on angiography hence the name moyamoya a Japanese word meaning puffy obscure or hazy like a puff of smoke
Stent assisted angioplasty in patients with Moyamoya disease mid term clinical and angiographic follow up results August 2012 Conference 22nd Meeting of the European Neurological Society 2012
The purpose of this study is to determine if people with moyamoya disease who have insufficient blood flow are at a higher risk for stroke. The Role of Cerebral Hemodynamics in Moyamoya Disease National Institute of Neurological Disorders and Stroke
Oct 30 2019 This study evaluated the strength of correlations between pre and post operative angiographic parameters and clinical status among paediatric patients with moyamoya. The participants included 58 patients of mean age 11 years at the time of surgery who underwent bilateral indirect revascularization in the same procedure at Boston Children’s
Nov 05 2015 Background and purpose Here we describe the clinical angiographic characteristics and long term surgical outcome of hemorrhagic moyamoya disease in children. Methods We retrospectively collected 374 consecutive children with moyamoya disease hemorrhagic 30 and ischemic 344 between 2004 and 2012 in our hospital. The clinical and
Feb 03 2022 Introduction Headache and anxiety are poorly described in children with moyamoya vasculopathy following revascularization. Hypothesis Headache and anxiety in pediatric moyamoya patients are common co morbidities and result in frequent healthcare utilization. Methods In this single center retrospective cohort study children <18 years of
Angiographic outcomes differed by surgical approach and were not associated with clinical outcomes. Literature identifying factors was sparse. Conclusions The existing literature indicates that factors such as cause degree of moyamoya vessels and surgical approach may affect the likelihood of Matsushima grade C revascularization in pediatric
On angiography these small blood vessels give off a puff of smoke appearance also known as MoyaMoya in Japanese . The disease is found more commonly in Asian countries and was first descried in Japanese literature in 1957. There is mounting evidence there is a genetic cause of the disease. Clinical Features
Dec 01 1997 Spontaneous occlusion of the circle of Willis moyamoya disease is a cerebrovascular disorder first described in the 1960s in Japan and remains a clinical entity with unknown etiology. 1 Since the Research Committee on Spontaneous Occlusion of the Circle of Willis Moyamoya Disease of the Ministry of Health and Welfare Japan RCMJ first
Moyamoya disease versus moyamoya syndrome Comparison of presentation and outcome in 338 hemispheres. James Feghali Risheng Xu Wuyang Yang Baseline demographic angiographic and clinical characteristics were compared between patients with MMS and MMD in addition to procedure related complications and length of stay LOS after surgery.
Clinical and angiographic outcomes from indirect revascularization surgery for Moyamoya disease in adults and children a review of 63 procedures. Neurosurgery 2011 68 34–43. doi 10.1227/NEU.0b013e3181fc5ec2
Improving indirect revascularization for effective treatment of adult moyamoya disease A prospective clinical cerebral angiographic and perfusion study. World Neurosurg e180 91. 24.
Oct 23 2021 Angiographic disease progression reportedly develops in adult moyamoya disease MMD . However more than half of patients analyzed underwent revascularization surgery. The present supplementary analysis of a 5 year prospective cohort with follow up using magnetic resonance angiography MRA and cerebral blood flow CBF measurements was to
Kuroda S Ishikawa T Houkin K Nanba R Hokari M Iwasaki Y. Incidence and clinical features of disease progression in adult moyamoya disease. Stroke 2005 36 Crossref